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Key Takeaways D51.0 is the billable ICD-10-CM code for vitamin B12 deficiency anemia due to intrinsic factor deficiency Synonyms include pernicious anemia, Addison anemia, Biermer anemia, and congenital pernicious anemia Requires confirmed intrinsic factor deficiency through lab testing or clinical diagnosis Falls under nutritional anemias category D50-D53 in ICD-10-CM classification system Documentation must specify intrinsic factor deficiency to avoid defaulting to D51.9 What Is ICD-10-CM Pernicious Anemia Code D51.0